Consilium MedicumConsilium MedicumConsilium MedicumConsilium Medicum2075-17532542-2170Consilium Medicum94431ArticlesСтатьиResearch ArticleHepatopulmonary syndromeГепатопульмональный синдромAvdeevS. NАвдеевСергей Николаевич

д-р мед. наук, проф., рук. клин. отд. ФГБУ НИИ пульмонологии

serg_avdeev@list.ruScientific-Research Institute of PulmonologyФГБУ НИИ пульмонологии ФМБА России15032016183VOL 18, NO3 (2016)ТОМ 18, №3 (2016)303528122021Copyright ©; 2016, Consilium MedicumCopyright ©; 2016, ООО "Консилиум Медикум"2016Consilium MedicumООО "Консилиум Медикум"https://creativecommons.org/licenses/by-nc-sa/4.0https://consilium.orscience.ru/2075-1753/article/view/94431

Hepatopulmonary syndrome (HPS) is a frequent complication of terminal liver disease. The HPS is based on the development of pulmonary vascular dilatation in response to the increase in the concentration of circulating vasoactive substances. To diagnose with HPS, the triad of symptoms is required: liver disease and/or portal hypertension, pulmonary vascular dilatation, and hypoxemia. The main therapeutic measures in HPS are the oxygen therapy and orthotopic liver transplantation.

Гепатопульмональный синдром (ГПС) является частым осложнением терминальных заболеваний печени. В основе ГПС лежит развитие дилатации легочных сосудов в ответ на повышение концентрации циркулирующих вазоактивных субстанций. Для постановки диагноза ГПС необходима триада признаков: заболевание печени и/или портальная гипертензия, дилатация легочных сосудов и гипоксемия. Основными лечебными мероприятиями при ГПС являются кислородотерапия и ортотопическая трансплантация печени.

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