Consilium MedicumConsilium Medicum2075-17532542-2170Consilium Medicum9685310.26442/20751753.2019.11.190687Research ArticleGranulomatosis with polyangiitis (Wegener's granulomatosis): variety of clinical and radiological manifestationsKorolevaIrina M.D. Sci. (Med.), Prof.mmact01@yandex.ruChichkovaNatalia V.D. Sci. (Med.), Prof.-SokolinaIrina A.Cand. Sci. (Med.)-BunchevaAnna V.Clinical Resident-Sechenov First Moscow State Medical University (Sechenov University)Moscow Scientific and Practical Center for Tuberculosis Control151120192111808519012022Copyright © 2019, Consilium Medicum2019Currently, the issue of radiation diagnosis of systemic vasculitis, clinical and radiological manifestations of which are very variable, remains relevant. There is a stable opinion about the traditional x-ray imaging of this heterogeneous group of diseases and the sequence of lesions of organs and systems. However, not always typical clinical and radiological symptoms are so "typically consistent" according to generally accepted scientific views, which significantly affects the timing of diagnosis and the appointment of adequate therapy, its results and, as a consequence, the quality of life of patients. Our article presents our own observations of 17 patients, including 7 men, 8 women and 2 children, who underwent a full range of clinical, laboratory and x-ray examinations, including the most modern diagnostic methods.systemic vasculitisgranulomatosis with polyangiitisWegener's granulomatosisantineutrophil cytoplasmic antibodiesANCA-associated vasculitismultispiral computed tomographybiopsyсистемные васкулитыгранулематоз с полиангиитомгранулематоз Вегенераантинейтрофильные цитоплазматические антителаАНЦА-ассоциированные васкулитымультиспиральная компьютерная томографиябиопсия[Бекетова Т.В. Современная классификация системных васкулитов. Клиницист. 2015; 2: 8-11.@@Beketova T.V. Sovremennaia klassifikatsiia sistemnykh vaskulitov. Klinitsist. 2015; 2: 8-11 (in Russian).][Нуднов Н.В., Шейх Г.Г., Кармазановский Г.Г. и др. Компьютерная томография в диагностике легочных поражений при гранулематозе с полиангиитом. Учебное пособие. М.: Крафт+, 2017. @@Nudnov N.V., Sheikh G.G., Karmazanovskii G.G. et al. Computed tomography in the diagnosis of pulmonary lesions in granulomatosis with polyangiitis. Tutorial. Moscow: Kraft, 2017 (in Russian).][Jennette J.C, Falk R.J, Bacon P.A et al. 2012 Revisied international Chapel Hill consensus conference nomenclature of vasculitides. Arthritis Rheum 2013; 65: 1-11.][Овсянников Д.Ю., Ильинская А.С., Ахвледиани С.Д. и др. Легочно-почечный синдром у детей: клиническое наблюдение гранулематоза с полиангиитом (Вегенера) и синдрома Гудпасчера. Педиатрия. 2015; 94 (4): 43-51.@@Ovsiannikov D.Iu., Il'inskaia A.S., Akhvlediani S.D. et al. Legochno-pochechnyi sindrom u detei: klinicheskoe nabliudenie granulematoza s poliangiitom (Vegenera) i sindroma Gudpaschera. Pediatriia. 2015; 94 (4): 43-51 (in Russian)][Brimo F, Lachapelle J, Epstein J.I. Testicular Vasculitis: A Series of 19 Cases. Urology 2011; 77: 1043-8.][Dufoir J-F, Le Gallou T, Cordier L-F et al. Urogenital Manifestationsin Wegener Granulomatosis. Medicine 2012; 91: 67-74.]